The Boy whose skin fell off

This is an excerpt out of the documentary called "The Boy whose skin fell off" Jonny Kennedy suffered from Epidermolysis bullosa (EB). It is an inherited connective tissue disease causing blisters in the skin and mucosal membranes, with an incidence of 1/50,000. Its severity ranges from mild to lethal.The skin is extremely fragile: minor mechanical friction or trauma will separate the layers of the skin and form blisters. People with this condition have an increased risk of cancers of the skin, and many will eventually be diagnosed with it as a complication of the chronic damage done to the skin. The skin has three layers; the outermost layer is the epidermis, and the middle layer is the dermis. In individuals with healthy skin, there are protein anchors between the layers that prevent them from moving independently from one another (shearing). In people born with EB, these top skin layers lack the protein anchors that hold them together, and any action that creates friction between them (like rubbing or pressure) will create blisters and painful sores. Sufferers of EB have compared the sores with third-degree burns (Source: Wikipedia) You can catch the whole documentary on Youtube. Poor guy finally died in his wheelchair while being filmed for the Documentary. I'm sure most Brits have already heard of this but to many Americans and other people this might be a new thing.